Idiopathic pulmonary fibrosis (I.P.F) is the most common type of pulmonary fibrosis.
I.P.F causes scarring (fibrosis) of the lungs for unknown reasons. The word “idiopathic” means it has no known cause. Over time the scarring gets worse and causes stiffness in the lungs. Making it difficult to breathe.
I.P.F primarily involves the interstitium. (the tissue and space around the air sacs of the lungs) There are many kinds of interstitial lung disease that can also cause inflammation and/or fibrosis, and these are all treated differently.
The damage caused to the lungs by I.P.F is currently irreversible and progressively gets worse over time. In some cases, it can be slowed by medications. People with I.P.F can also be recommended for lung transplant.
It is recommended that I.P.F patients stay active, eat well, and use oxygen therapy as prescribed to help manage their I.P.F.
I.P.F is considered a rare, sporadic disease. According to the National Institutes of Health, about 100,000 people in the United States have I.P.F, and approximately 30,000 to 40,000 new cases are found each year. Worldwide, I.P.F affects 13 to 20 out of every 100,000 people.
relating to or denoting any disease or condition that arises spontaneously or for which the cause is unknown.
relating to the lungs. “pulmonary blood flow”
the thickening and scarring of connective tissue.
an abnormally low concentration of oxygen in the blood. (oxygen deficiency)
of, forming, or occupying interstices (space between structures or objects)
(of an illness) persisting for a long time or constantly recurring.